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PLATELET DISORDERS
37問 • 2年前
  • Yves Laure Pimentel
    • 通報

    問題一覧

  • 1

    Bernard Soulier Syndrome (BSS) deficiency of

    GP Ib/IX/V

  • 2

    Bernard Soulier Syndrome (BSS) inherited as

    autosomal recessive

  • 3

    associated with decreased plt. ct. Giant platelet normal ACE ABNORMAL AGGREGATION IN RISTOCETIN

    Bernard Soulier Syndrome (BSS)

  • 4

    process where in platelets adhere to a foreign surface

    Platelet Adhesion

  • 5

    Platelet Adhesion important in this process are:

    GP IB/IX/V VWF

  • 6

    primary platelet surface receptor for VWF

    GP IB/IX/V

  • 7

    ligand of GpIB/IX/V

    VWF

  • 8

    generally described as the deficiency of VWF

    VON WILLEBRAND'S DISEASE (VWD)

  • 9

    VON WILLEBRAND'S DISEASE (VWD) inherited as

    AUTOSOMAL DOMINANT

  • 10

    general characteristics: decreased factor VIII NORMAL PT, PROLONGED APTT NORMAL AGGREGATION: A,C,E ABNORMAL AGGREGATION: RISTOCETIN

    VON WILLEBRAND'S DISEASE (VWD)

  • 11

    most common variant of VWD mildest form

    VWD TYPE 1

  • 12

    rarest type of VWD MOST SEVERE FORM OF VWD

    VWD TYPE III

  • 13

    VWD TYPE I BLEEDING TIME: BLEEDING TENDENCY: PETECHIAE:

    normal or increased mild none

  • 14

    VWD TYPE II BLEEDING TIME: BLEEDING TENDENCY: PETECHIAE:

    increased moderate usually none

  • 15

    VWD TYPE III BLEEDING TIME: BLEEDING TENDENCY: PETECHIAE:

    increased often severe occasionally

  • 16

    examples of conditions with PLATELET ADHESION DISORDER

    BSS VWD

  • 17

    examples of conditions with PLATELET AGGREGATION DISORDER

    GLANZMANN'S THROMBASTHENIA

  • 18

    GLANZMANN'S THROMBASTHENIA deficiency of

    GP IIB/IIIA

  • 19

    GLANZMANN'S THROMBASTHENIA inherited as

    autosomal recessive

  • 20

    process wherein Platelets adhere to other platelets

    platelet aggregation

  • 21

    platelet aggregation important in this process

    GP IIB/IIIA FIBRINOGEN

  • 22

    platelet fibrinogen receptor

    GP IIB/IIIA

  • 23

    bridge or linked of Platelet to have aggregation

    fibrinogen

  • 24

    absence of fibrinogen in blood

    Hereditary afibrinogenemia

  • 25

    Characterized by: very prolonged BT ABN clot retraction ABN aggregation response in A, C, E normal aggregation response in RISTOCETIN

    GLANZMANN'S THROMBASTHENIA

  • 26

    reduced levels fibrinogen in the blood

    hypofibrinogenemia

  • 27

    fibrinogen does not function normally on optimally

    dysfibrinogenemia

  • 28

    examples of conditions with PLATELET SECRETION DISORDER

    thromboxane pathway disorders Cyclooxygenase or thromboxane synthetase deficiency storage pool diseases Alpha granules deficiency Dense granule deficiencies

  • 29

    Alpha granules deficiency

    Gray platelet syndrome

  • 30

    Gray platelet syndrome

    Alpha granules deficiency

  • 31

    Dense Granule deficiencies

    Hermansky- Pudlak syndrome Chediak- Higashi syndrome TAR syndrome Wiskott-Aldrich syndrome

  • 32

    Hermansky- Pudlak syndrome Inheritance pattern Albinism Platelet count

    AR OCULOCUTANEOUS ALBINISM NORMAL

  • 33

    Chediak- Higashi syndrome Inheritance pattern Albinism Platelet count

    AR PARTIAL ALBINISM LOW

  • 34

    Wiskott-Aldrich syndrome Inheritance pattern Albinism Platelet count

    X linked recessive No albinism Low

  • 35

    TAR syndrome Inheritance pattern Albinism Platelet count

    AR NO ALBINISM NORMAL

  • 36

    TAR SYNDROME INFANCY PLATELET COUNT

    low

  • 37

    TAR SYNDROME WITHIN 1 YEAR OF BIRTH PLATELET COUNT

    normal

    • other names parasitology

    other names parasitology

    Yves Laure Pimentel · 70問 · 2年前

    other names parasitology

    other names parasitology

    70問 • 2年前
    Yves Laure Pimentel

    PARASITOLOGY

    PARASITOLOGY

    Yves Laure Pimentel · 111問 · 2年前

    PARASITOLOGY

    PARASITOLOGY

    111問 • 2年前
    Yves Laure Pimentel

    HTMLBE

    HTMLBE

    Yves Laure Pimentel · 64問 · 2年前

    HTMLBE

    HTMLBE

    64問 • 2年前
    Yves Laure Pimentel

    CC - 1 LAB. SAFETY, BASIC UNITS, AND CONVERSION FACTOR

    CC - 1 LAB. SAFETY, BASIC UNITS, AND CONVERSION FACTOR

    Yves Laure Pimentel · 61問 · 2年前

    CC - 1 LAB. SAFETY, BASIC UNITS, AND CONVERSION FACTOR

    CC - 1 LAB. SAFETY, BASIC UNITS, AND CONVERSION FACTOR

    61問 • 2年前
    Yves Laure Pimentel

    HISTOPATHOLOGY

    HISTOPATHOLOGY

    Yves Laure Pimentel · 69問 · 2年前

    HISTOPATHOLOGY

    HISTOPATHOLOGY

    69問 • 2年前
    Yves Laure Pimentel

    CC-2 SPECTROPHOTOMETRY

    CC-2 SPECTROPHOTOMETRY

    Yves Laure Pimentel · 100問 · 2年前

    CC-2 SPECTROPHOTOMETRY

    CC-2 SPECTROPHOTOMETRY

    100問 • 2年前
    Yves Laure Pimentel

    CC-3 ELECTROPHORESIS

    CC-3 ELECTROPHORESIS

    Yves Laure Pimentel · 41問 · 2年前

    CC-3 ELECTROPHORESIS

    CC-3 ELECTROPHORESIS

    41問 • 2年前
    Yves Laure Pimentel

    AUBF LAB SAFETY

    AUBF LAB SAFETY

    Yves Laure Pimentel · 87問 · 2年前

    AUBF LAB SAFETY

    AUBF LAB SAFETY

    87問 • 2年前
    Yves Laure Pimentel

    CSF 1

    CSF 1

    Yves Laure Pimentel · 100問 · 2年前

    CSF 1

    CSF 1

    100問 • 2年前
    Yves Laure Pimentel

    CSF 2

    CSF 2

    Yves Laure Pimentel · 82問 · 2年前

    CSF 2

    CSF 2

    82問 • 2年前
    Yves Laure Pimentel

    SEMEN 1

    SEMEN 1

    Yves Laure Pimentel · 100問 · 2年前

    SEMEN 1

    SEMEN 1

    100問 • 2年前
    Yves Laure Pimentel

    SEMEN 2

    SEMEN 2

    Yves Laure Pimentel · 7問 · 2年前

    SEMEN 2

    SEMEN 2

    7問 • 2年前
    Yves Laure Pimentel

    SYNOVIAL FLUID 1

    SYNOVIAL FLUID 1

    Yves Laure Pimentel · 100問 · 2年前

    SYNOVIAL FLUID 1

    SYNOVIAL FLUID 1

    100問 • 2年前
    Yves Laure Pimentel

    SYNOVIAL FLUID 2

    SYNOVIAL FLUID 2

    Yves Laure Pimentel · 6問 · 2年前

    SYNOVIAL FLUID 2

    SYNOVIAL FLUID 2

    6問 • 2年前
    Yves Laure Pimentel

    SEROUS FLUID

    SEROUS FLUID

    Yves Laure Pimentel · 25問 · 2年前

    SEROUS FLUID

    SEROUS FLUID

    25問 • 2年前
    Yves Laure Pimentel

    PLEURAL FLUID

    PLEURAL FLUID

    Yves Laure Pimentel · 44問 · 2年前

    PLEURAL FLUID

    PLEURAL FLUID

    44問 • 2年前
    Yves Laure Pimentel

    PERICARDIAL FLUID

    PERICARDIAL FLUID

    Yves Laure Pimentel · 18問 · 2年前

    PERICARDIAL FLUID

    PERICARDIAL FLUID

    18問 • 2年前
    Yves Laure Pimentel

    PERITONEAL FLUID/ ASCITIC FLUID

    PERITONEAL FLUID/ ASCITIC FLUID

    Yves Laure Pimentel · 30問 · 2年前

    PERITONEAL FLUID/ ASCITIC FLUID

    PERITONEAL FLUID/ ASCITIC FLUID

    30問 • 2年前
    Yves Laure Pimentel

    AMNIOTIC FLUID

    AMNIOTIC FLUID

    Yves Laure Pimentel · 92問 · 2年前

    AMNIOTIC FLUID

    AMNIOTIC FLUID

    92問 • 2年前
    Yves Laure Pimentel

    FECALYSIS

    FECALYSIS

    Yves Laure Pimentel · 80問 · 2年前

    FECALYSIS

    FECALYSIS

    80問 • 2年前
    Yves Laure Pimentel

    問題一覧

  • 1

    Bernard Soulier Syndrome (BSS) deficiency of

    GP Ib/IX/V

  • 2

    Bernard Soulier Syndrome (BSS) inherited as

    autosomal recessive

  • 3

    associated with decreased plt. ct. Giant platelet normal ACE ABNORMAL AGGREGATION IN RISTOCETIN

    Bernard Soulier Syndrome (BSS)

  • 4

    process where in platelets adhere to a foreign surface

    Platelet Adhesion

  • 5

    Platelet Adhesion important in this process are:

    GP IB/IX/V VWF

  • 6

    primary platelet surface receptor for VWF

    GP IB/IX/V

  • 7

    ligand of GpIB/IX/V

    VWF

  • 8

    generally described as the deficiency of VWF

    VON WILLEBRAND'S DISEASE (VWD)

  • 9

    VON WILLEBRAND'S DISEASE (VWD) inherited as

    AUTOSOMAL DOMINANT

  • 10

    general characteristics: decreased factor VIII NORMAL PT, PROLONGED APTT NORMAL AGGREGATION: A,C,E ABNORMAL AGGREGATION: RISTOCETIN

    VON WILLEBRAND'S DISEASE (VWD)

  • 11

    most common variant of VWD mildest form

    VWD TYPE 1

  • 12

    rarest type of VWD MOST SEVERE FORM OF VWD

    VWD TYPE III

  • 13

    VWD TYPE I BLEEDING TIME: BLEEDING TENDENCY: PETECHIAE:

    normal or increased mild none

  • 14

    VWD TYPE II BLEEDING TIME: BLEEDING TENDENCY: PETECHIAE:

    increased moderate usually none

  • 15

    VWD TYPE III BLEEDING TIME: BLEEDING TENDENCY: PETECHIAE:

    increased often severe occasionally

  • 16

    examples of conditions with PLATELET ADHESION DISORDER

    BSS VWD

  • 17

    examples of conditions with PLATELET AGGREGATION DISORDER

    GLANZMANN'S THROMBASTHENIA

  • 18

    GLANZMANN'S THROMBASTHENIA deficiency of

    GP IIB/IIIA

  • 19

    GLANZMANN'S THROMBASTHENIA inherited as

    autosomal recessive

  • 20

    process wherein Platelets adhere to other platelets

    platelet aggregation

  • 21

    platelet aggregation important in this process

    GP IIB/IIIA FIBRINOGEN

  • 22

    platelet fibrinogen receptor

    GP IIB/IIIA

  • 23

    bridge or linked of Platelet to have aggregation

    fibrinogen

  • 24

    absence of fibrinogen in blood

    Hereditary afibrinogenemia

  • 25

    Characterized by: very prolonged BT ABN clot retraction ABN aggregation response in A, C, E normal aggregation response in RISTOCETIN

    GLANZMANN'S THROMBASTHENIA

  • 26

    reduced levels fibrinogen in the blood

    hypofibrinogenemia

  • 27

    fibrinogen does not function normally on optimally

    dysfibrinogenemia

  • 28

    examples of conditions with PLATELET SECRETION DISORDER

    thromboxane pathway disorders Cyclooxygenase or thromboxane synthetase deficiency storage pool diseases Alpha granules deficiency Dense granule deficiencies

  • 29

    Alpha granules deficiency

    Gray platelet syndrome

  • 30

    Gray platelet syndrome

    Alpha granules deficiency

  • 31

    Dense Granule deficiencies

    Hermansky- Pudlak syndrome Chediak- Higashi syndrome TAR syndrome Wiskott-Aldrich syndrome

  • 32

    Hermansky- Pudlak syndrome Inheritance pattern Albinism Platelet count

    AR OCULOCUTANEOUS ALBINISM NORMAL

  • 33

    Chediak- Higashi syndrome Inheritance pattern Albinism Platelet count

    AR PARTIAL ALBINISM LOW

  • 34

    Wiskott-Aldrich syndrome Inheritance pattern Albinism Platelet count

    X linked recessive No albinism Low

  • 35

    TAR syndrome Inheritance pattern Albinism Platelet count

    AR NO ALBINISM NORMAL

  • 36

    TAR SYNDROME INFANCY PLATELET COUNT

    low

  • 37

    TAR SYNDROME WITHIN 1 YEAR OF BIRTH PLATELET COUNT

    normal