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MINOR LIPOPROTEINS
63問 • 2年前
  • Yves Laure Pimentel
  • 通報

    問題一覧

  • 1

    Minor Lipoproteins ARE

    Lipoprotein A /Lpa Intermediate Density Lipoprotein (IDL)

  • 2

    Lipoprotein A /Lpa _______ pre –B lipoprotein

    SINKING

  • 3

    It involved accumulation of plasma VLDL rich in cholesterol and chylomicrons remnants

    Familial Dysbetalipoproteinemia/ Type 3 Hyperlipoproteinemia

  • 4

    Reference value VLDL C/TAG ratio:

    0.2

  • 5

    composed primarily of cholesterol esters, phospholipids, and apolipoprotein (a) and Apo B100

    Lipoprotein A /Lpa

  • 6

    INDEPENDENT risk factor for atherosclerosis

    Lipoprotein A /Lpa

  • 7

    Abetalipoproteinemia a. defective ______synthesis

    APO B

  • 8

    Lipoprotein A /Lpa _____ risk factor for atherosclerosis

    INDEPENDENT

  • 9

    defective APO B synthesis

    Abetalipoproteinemia

  • 10

    VLDL, LDL, and Chylomicrons= ABSENT

    Abetalipoproteinemia

  • 11

    Lipoprotein A /Lpa IS similar to

    plasminogen

  • 12

    Elevated levels of Lp(a) are associated with

    increased risk for coronary heart disease, myocardial infarction, and cerebrovascular disease

  • 13

    = ARE ABSENTIN Abetalipoproteinemia

    VLDL, LDL, and Chylomicrons

  • 14

    – VLDL catabolic prod.

    Intermediate Density Lipoprotein (IDL)

  • 15

    defective APO B synthesis

    Abetalipoproteinemia

  • 16

    Abetalipoproteinemia defective APO B synthesis/?

    BASSEN KORNZHEIG

  • 17

    Intermediate Density Lipoprotein (IDL) – is catabolic prod. of?

    VLDL

  • 18

    Chole and TAG = low

    Abetalipoproteinemia

  • 19

    is a transitional form

    Intermediate Density Lipoprotein (IDL)

  • 20

    Abetalipoproteinemia Chole and TAG = ?

    low

  • 21

    (IDL) –Carry: endogenous __________and cholesterol esters

    TAG

  • 22

    apo –B deficiency

    Hypobetalipoproteinemia

  • 23

    (IDL) –apolipoproteins

    apolipoproteins B-100

  • 24

    LDL-chole and total cholesterol = low levels VLDL-chole and Total TAG =Low or normal

    Hypobetalipoproteinemia

  • 25

    Abnormal Lipoproteins

    Lipoprotein X B –VLDL (floating B lipoprotein)

  • 26

    increased IDL DSE

    TYPE III HYPERLIPOPROTENEMIA

  • 27

    Hypoalphalipoproteinemia: Severely elevated __________level and____ HDL level

    TAG; LOW

  • 28

    : Severely elevated TAG level and LOW HDL level

    Hypoalphalipoproteinemia

  • 29

    Specific and sensitive indicator of cholestasis

    Lipoprotein X

  • 30

    Tangier’s disease - _____________________due to mutation in the ABCA1

    COMPLETE ABSENCE OF HDL

  • 31

    Lipoprotein X Specific and sensitive indicator of

    cholestasis

  • 32

    Lipoprotein X deficiency

    OBSTRUCTIVE jaundice and LCAT deficiency

  • 33

    - COMPLETE ABSENCE OF HDL due to mutation in the ABCA1

    Tangier’s disease

  • 34

    Lecithin Cholesterol Acyl Transferase (LCAT) deficiency – ______ disease

    FISHEY

  • 35

    WHAT Abnormal Lipoproteins THAT HAS OBSTRUCTIVE jaundice and LCAT deficiency

    Lipoprotein X

  • 36

    “abnormally migrating B-VLDL”

    B –VLDL (floating B lipoprotein

  • 37

    WHAT deficiency – FISHEY disease

    Lecithin Cholesterol Acyl Transferase (LCAT)

  • 38

    B –VLDL (floating B lipoprotein IS ALSO CALLED

    “abnormally migrating B-VLDL”

  • 39

    - deficiency of the enzyme hexosaminidase A- Spingolipid accum.

    Tay –Sach’s Disease

  • 40

    Tay –Sach’s Disease - deficiency of the ? - Spingolipid accum.

    enzyme hexosaminidase A

  • 41

    B –VLDL (floating B lipoprotein) ALSO FOUND IN WHAT DISEASES?

    dysbetalipoproteinemia/ type 3-hyperlipoprotenenmia

  • 42

    Found in dysbetalipoproteinemia/ type 3-hyperlipoprotenenmia

    B –VLDL (floating B lipoprotein)

  • 43

    Associated to Coronary disease

    ALL EXCEPT 1

  • 44

    Eruptive xanthoma

    TYPE 1,3,5

  • 45

    Xanthelasma and Hypercholesterolemia

    TYPE 2

  • 46

    Pancreatitis

    TYPE 1 & 5

  • 47

    DOMINANT CARRIER OF CHOLESTEROL TO TISSUES

    VLDL AND LDL

  • 48

    Familial Hypercholesterolemia (Type 2a) a. Defective ____receptors

    LDL

  • 49

    Defective LDL receptors

    Familial Hypercholesterolemia (Type 2a)

  • 50

    WHAT TYPE: Chylomicrons

    1

  • 51

    WHAT TYPE: LDL

    2A

  • 52

    WHAT TYPE: LDL and VLDL

    2b

  • 53

    WHAT TYPE: IDL

    3

  • 54

    WHAT TYPE: VLDL

    4

  • 55

    WHAT TYPE: VLDL , Chylomicron

    5

  • 56

    Type 1

    Chylomicrons

  • 57

    Type 2a

    LDL

  • 58

    Type 2b

    LDL and VLDL

  • 59

    Type 3

    IDL

  • 60

    Type 4

    VLDL

  • 61

    Type 5

    VLDL, Chylomicron

  • 62

    TC and LDL C (2-3x above normal)

    Familial Hypercholesterolemia (Type 2a)

  • 63

    : a broad abnormal BAND between VLDL and LDL (B-VLDL)

    Familial Dysbetalipoproteinemia/ Type 3 Hyperlipoproteinemia

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    CSF 1

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    CSF 1

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    CSF 2

    CSF 2

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    SEMEN 1

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    SEMEN 2

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    PLEURAL FLUID

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    PERICARDIAL FLUID

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    問題一覧

  • 1

    Minor Lipoproteins ARE

    Lipoprotein A /Lpa Intermediate Density Lipoprotein (IDL)

  • 2

    Lipoprotein A /Lpa _______ pre –B lipoprotein

    SINKING

  • 3

    It involved accumulation of plasma VLDL rich in cholesterol and chylomicrons remnants

    Familial Dysbetalipoproteinemia/ Type 3 Hyperlipoproteinemia

  • 4

    Reference value VLDL C/TAG ratio:

    0.2

  • 5

    composed primarily of cholesterol esters, phospholipids, and apolipoprotein (a) and Apo B100

    Lipoprotein A /Lpa

  • 6

    INDEPENDENT risk factor for atherosclerosis

    Lipoprotein A /Lpa

  • 7

    Abetalipoproteinemia a. defective ______synthesis

    APO B

  • 8

    Lipoprotein A /Lpa _____ risk factor for atherosclerosis

    INDEPENDENT

  • 9

    defective APO B synthesis

    Abetalipoproteinemia

  • 10

    VLDL, LDL, and Chylomicrons= ABSENT

    Abetalipoproteinemia

  • 11

    Lipoprotein A /Lpa IS similar to

    plasminogen

  • 12

    Elevated levels of Lp(a) are associated with

    increased risk for coronary heart disease, myocardial infarction, and cerebrovascular disease

  • 13

    = ARE ABSENTIN Abetalipoproteinemia

    VLDL, LDL, and Chylomicrons

  • 14

    – VLDL catabolic prod.

    Intermediate Density Lipoprotein (IDL)

  • 15

    defective APO B synthesis

    Abetalipoproteinemia

  • 16

    Abetalipoproteinemia defective APO B synthesis/?

    BASSEN KORNZHEIG

  • 17

    Intermediate Density Lipoprotein (IDL) – is catabolic prod. of?

    VLDL

  • 18

    Chole and TAG = low

    Abetalipoproteinemia

  • 19

    is a transitional form

    Intermediate Density Lipoprotein (IDL)

  • 20

    Abetalipoproteinemia Chole and TAG = ?

    low

  • 21

    (IDL) –Carry: endogenous __________and cholesterol esters

    TAG

  • 22

    apo –B deficiency

    Hypobetalipoproteinemia

  • 23

    (IDL) –apolipoproteins

    apolipoproteins B-100

  • 24

    LDL-chole and total cholesterol = low levels VLDL-chole and Total TAG =Low or normal

    Hypobetalipoproteinemia

  • 25

    Abnormal Lipoproteins

    Lipoprotein X B –VLDL (floating B lipoprotein)

  • 26

    increased IDL DSE

    TYPE III HYPERLIPOPROTENEMIA

  • 27

    Hypoalphalipoproteinemia: Severely elevated __________level and____ HDL level

    TAG; LOW

  • 28

    : Severely elevated TAG level and LOW HDL level

    Hypoalphalipoproteinemia

  • 29

    Specific and sensitive indicator of cholestasis

    Lipoprotein X

  • 30

    Tangier’s disease - _____________________due to mutation in the ABCA1

    COMPLETE ABSENCE OF HDL

  • 31

    Lipoprotein X Specific and sensitive indicator of

    cholestasis

  • 32

    Lipoprotein X deficiency

    OBSTRUCTIVE jaundice and LCAT deficiency

  • 33

    - COMPLETE ABSENCE OF HDL due to mutation in the ABCA1

    Tangier’s disease

  • 34

    Lecithin Cholesterol Acyl Transferase (LCAT) deficiency – ______ disease

    FISHEY

  • 35

    WHAT Abnormal Lipoproteins THAT HAS OBSTRUCTIVE jaundice and LCAT deficiency

    Lipoprotein X

  • 36

    “abnormally migrating B-VLDL”

    B –VLDL (floating B lipoprotein

  • 37

    WHAT deficiency – FISHEY disease

    Lecithin Cholesterol Acyl Transferase (LCAT)

  • 38

    B –VLDL (floating B lipoprotein IS ALSO CALLED

    “abnormally migrating B-VLDL”

  • 39

    - deficiency of the enzyme hexosaminidase A- Spingolipid accum.

    Tay –Sach’s Disease

  • 40

    Tay –Sach’s Disease - deficiency of the ? - Spingolipid accum.

    enzyme hexosaminidase A

  • 41

    B –VLDL (floating B lipoprotein) ALSO FOUND IN WHAT DISEASES?

    dysbetalipoproteinemia/ type 3-hyperlipoprotenenmia

  • 42

    Found in dysbetalipoproteinemia/ type 3-hyperlipoprotenenmia

    B –VLDL (floating B lipoprotein)

  • 43

    Associated to Coronary disease

    ALL EXCEPT 1

  • 44

    Eruptive xanthoma

    TYPE 1,3,5

  • 45

    Xanthelasma and Hypercholesterolemia

    TYPE 2

  • 46

    Pancreatitis

    TYPE 1 & 5

  • 47

    DOMINANT CARRIER OF CHOLESTEROL TO TISSUES

    VLDL AND LDL

  • 48

    Familial Hypercholesterolemia (Type 2a) a. Defective ____receptors

    LDL

  • 49

    Defective LDL receptors

    Familial Hypercholesterolemia (Type 2a)

  • 50

    WHAT TYPE: Chylomicrons

    1

  • 51

    WHAT TYPE: LDL

    2A

  • 52

    WHAT TYPE: LDL and VLDL

    2b

  • 53

    WHAT TYPE: IDL

    3

  • 54

    WHAT TYPE: VLDL

    4

  • 55

    WHAT TYPE: VLDL , Chylomicron

    5

  • 56

    Type 1

    Chylomicrons

  • 57

    Type 2a

    LDL

  • 58

    Type 2b

    LDL and VLDL

  • 59

    Type 3

    IDL

  • 60

    Type 4

    VLDL

  • 61

    Type 5

    VLDL, Chylomicron

  • 62

    TC and LDL C (2-3x above normal)

    Familial Hypercholesterolemia (Type 2a)

  • 63

    : a broad abnormal BAND between VLDL and LDL (B-VLDL)

    Familial Dysbetalipoproteinemia/ Type 3 Hyperlipoproteinemia