èšæ¶åºŠ
6å
17å
0å
0å
0å
ã¢ã«ãŠã³ãç»é²ããŠãè§£ççµæãä¿åããã
åé¡äžèЧ
1
ãã¢ãã³ïŒãã¿ãã³B1ïŒ
2
ããªããã·ã³ïŒãã¿ãã³B6ïŒ
3
ã¢ã¹ã³ã«ãã³é žïŒãã¿ãã³CïŒ
4
ããªãã³
5
ãã³ããã³é žïŒCoAã®æ§ææåïŒ
6
ãã¿ãã³B12ïŒã³ãã©ãã³ïŒð©ðª
7
ãã£ãããã³ïŒãã¿ãã³KïŒ
8
ãªããã©ãã³ïŒãã¿ãã³B2ïŒ
9
èé žïŒãããã€ã«ã°ã«ã¿ãã³é žïŒ
10
ãã€ã¢ã·ã³ïŒãã³ãã³é žããã³ãã³ã¢ããïŒ
11
ãã³ãã§ããŒã«ïŒãã¿ãã³EïŒ
12
ãšã«ãŽã«ã«ã·ãã§ããŒã«ïŒãã¿ãã³DïŒ
13
ã¬ãããŒã«ïŒãã¿ãã³AïŒ
14
æ«æ¢¢ç¥çµé害
èæ°ïŒãã¿ãã³B1ïŒ
15
ãã©ãã³ãã¢ããããã¯ã¬ãªãã
FAD
16
NADã®é žååã¯ïŒ
NADïŒ
17
ãã©ã°ã©ã£ãŠïŒ
èªç¥ç
18
èé žð±ååç©å
ãããã€ã«ã°ã«ã¿ãã³é ž
19
ããã©ãããèé ž
THF
20
ç¹ç°çãªçµåã¿ã³ãã¯è³ªïŒãã¿ãã³B12ð©ïŒ
ãããã³ãªã³ïŒå å å ã³ãã©ãã³ã®è žç®¡åžåãšè¡æ¶²èŒžéð©žã¯ããããä»ããŠè¡ããã
21
ãã¿ãã³B12ã®ãæ¬ ä¹çã
å·šèµ€èœæ§è²§è¡ïŒð±èé žæ¬ ä¹çãèµ·ããããïŒïŒ
22
ð§ð»äººãå«ãéé·é¡ã¯ãåæçµè·¯ã®æçµæ®µéã®é µçŽ ã§ããïŒãïŒéºäŒåãå€ç°ããŠããããã ãã¿ãã³Cãåæã§ããªãð£
L-ã°ãã-γã©ã¯ãã³ãªãã·ããŒãŒ
23
ã¬ãããŒã«ã¯äœåïŒ
ã¢ã«ã³ãŒã«åã CH2OH ã®o-ããão-ã
24
ã¬ãããŒã«ã¯äœåïŒ
ã¢ã«ãããåã CHO ãªããŒããâ¡ïž
25
ã¬ããã€ã³é žã¯äœåïŒ
ã«ã«ãã³é žåãã COOH
26
ðïžããªãã·ã³ãã¯ãïŒãïŒãšçµåããŠãïŒãïŒã«ãªãã
ã¬ãããŒã«, ãããã·ã³
27
ã¬ããã€ã³é žïŒãã¿ãã³AïŒ
βã«ããã³ïŒåé§äœïŒâ¡ïžã¬ãããŒã«â¡ïžå€§éšåã¯ã¬ããã€ã³é ž, ããªã¢æ©èœãæ£åžžã«ä¿ã€
28
ãã¿ãã³E ïŒäžé£œåçµåããªãâïŒ
ãã³ãã§ããŒã«
29
ãã¿ãã³E ïŒäžé£œåçµåãããâïžïŒ
ãã³ããªãšããŒã«ðŠïŒåŽéã«äºéçµåããïŒ Eè¯ããšãåãâŒïž
30
ãã¿ãã³DïŒåç©èµ·æºïŒ
D3 ã³ã¬ã«ã«ã·ãã§ããŒã«
31
èæ°ãã¯ã©ã®ãã¿ãã³ïŒ
ãã¿ãã³B1
32
ãã¿ãã³K ååç©
ãã£ãããã³
33
ã¡ãã«ã³ãã©ãã³ïŒãã¿ãã³12ïŒã¯ãïŒããïŒã®è£é µçŽ
ã¡ããªãã³ã·ã³ã¿ãŒãŒ
34
ã¢ããã·ã«ã³ãã©ãã³ïŒãã¿ãã³12ïŒã¯ãïŒããïŒã®è£é µçŽ
ã¡ãã«ãããã«CoAã ã¿ãŒãŒð
35
ç²ç¶è ºããåæ³ããããPTH-ãã¿ãã³Dç³»ãæå¶ããðŠ
ã«ã«ã·ããã³ïŒCTïŒ
36
ãã³ããã³é žïŒããªãã³ïŒãã€ã¢ã·ã³ã¯ãïŒãïŒãšïŒãïŒã®ä»£è¬ã«é¢äž
ç³è³ª, è質
37
æ¬ ä¹ïŒè±æ¯ðð»ââïžãç®èç
ããªãã³
38
ACC
ã¢ã»ãã«CoAã«ã«ããã·ã©ãŒãŒ
39
ãã¿ãã³K1
ãã£ãããã³
40
ãã¿ãã³K2
ã¡ãããã³
41
è¡äžãŠã¯ãTTRãšçµåããŠã ïŒã¬ãããŒã«ã»ãããïŒè€åäœãšããŠåŸªç°ðãã
ã¬ãããŒã«ã»RBPã»TTR
42
ïŒéå°çïŒèå ã®å¥åœ¢ð¶ð»ãé èå å§äº¢é²ã«ããé ç
ãã¿ãã³A
43
ãããã¿ãã³D2
ãšã«ãŽã¹ãããŒã«